先天性囊狀腺樣畸形是一種不尋常的肺部畸形發育。其特色是肺部的正常組織由含有囊狀、固形或混合病變等特殊組織結構所取代。苦罹患先天性肺囊狀腺樣畸形時，在新生嬰兒其出現的臨床表征是以畸形病變壓迫肺部組織而造成進行性的呼吸窘迫?特色。但在幼兒與大小孩則是以反復性的呼吸道感染表現?主。而以肺膿瘍作?急性表征者則是非常罕見。我們報告一例八歲女孩罹患先天性肺囊狀腺樣畸形且以肺膿瘍作?急性表征。
Congenital cystic adenomatoid malformation (CCAM) of the lung is an uncommon anomaly of fetal development of terminal respiratory structures. Patients with CCAM may present either in the newborn with progressive respiratory distress, or in older children with recurrent pulmonary infections. Lung abscess is an extremely rare presentation. Herein we report an 8-year-old girl with type 1 CCAM who presented as lung abscess.
