Right-sided congenital diaphragmatic hernia is a rare clinical condition that often presents in the neonatal period. It is important to make a differential diagnosis and decide on a clinical course for treating this condition as quickly as possible. We report a newborn with respiratory distress initially thought to be related to pneumothorax. The definite diagnosis of right-sided congenital diaphragmatic hernia was made following further imaging studies. Chest ultrasound may be helpful for preventing misdiagnosis. We also discuss the proper management of right-sided congenital diaphragmatic hernia.